Ebstein's anomaly associated with splenomegaly and reversible hypersplenism.
نویسندگان
چکیده
A case of Ebstein's anomaly associated with chronic right heart failure, hepatosplenomegaly, and the haematological features of hypersplenism is presented. The haematological abnormalities were corrected after tricuspid valve replacement but recurred with the reemergence of clinical features of right heart failure.
منابع مشابه
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Introduction: Ebstein's anomaly (EA) is a rare congenital malformation of the tricuspid valve, often associated with PFO, which is present in 80-90% of patients & predisposes to para-doxical embolization. Case Report: The case described was a 30 year old female, in the post partum phase, (ten days after normal vaginal delivery) who was presented to the emergency department with seizure & Rt s...
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ورودعنوان ژورنال:
- British heart journal
دوره 65 4 شماره
صفحات -
تاریخ انتشار 1991